Background

Condition Lookup

Number of Conditions: 1

Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)

Specialty: Nose and Throat

Category: Nasal Conditions

Sub-category: Autoimmune and Systemic Conditions

Symptoms:
chronic sinusitis; nasal ulcerations; nasal discharge (often bloody); facial pain; fatigue; weight loss; cough; hemoptysis (coughing up blood); joint pain

Root Cause:
An autoimmune condition that causes inflammation of blood vessels (vasculitis) and granulomas in the respiratory tract, kidneys, and other organs.

How it's Diagnosed: videos
Diagnosis is based on clinical symptoms, laboratory tests (e.g., c-ANCA), and biopsy of affected tissues showing granulomatous inflammation and vasculitis.

Treatment:
Treatment involves immunosuppressive drugs such as corticosteroids (e.g., prednisone) and cytotoxic agents (e.g., cyclophosphamide). Maintenance therapy may include methotrexate or rituximab.

Medications:
Corticosteroids (e.g., prednisone ) are used as anti-inflammatory agents, while cytotoxic agents like cyclophosphamide (alkylating agents) suppress the immune response. Methotrexate (antimetabolite) and rituximab (monoclonal antibody) may be used for maintenance therapy.

Prevalence: How common the health condition is within a specific population.
A rare condition, affecting approximately 3-4 people per million annually.

Risk Factors: Factors or behaviors that increase the likelihood of developing the condition.
Genetic predisposition, environmental triggers (e.g., infections), and smoking.

Prognosis: The expected outcome or course of the condition over time.
With treatment, the prognosis has improved, but long-term management is required to prevent relapses and complications.

Complications: Additional problems or conditions that may arise as a result of the original condition.
Kidney failure, hearing loss, pulmonary hemorrhage, and the development of other systemic organ failures.